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1
題名:
FAMILIAL EXUDATIVE VITREORETINOPATHYA──CASE REPORT
(12點)
病例報告──家族滲出性玻璃體視網膜病變
著者:
Chun-Pin Tsai
(
蔡俊斌
) ;
Der-Chong Tsai
(
蔡德中
) ;
Ling-Ing Lau
(
劉伶瑛
) ;
Fenq-Lih Lee
(
李鳳利
) ;
Wen-Ming Hsu
(
許紋銘
)
出版地區:
台灣
出版城市:
台北市
學科:
醫學綜合
關鍵字:
familial exudative vitreoretinopathy
;
FEVR
;
subretinal fibrosis
刊名:
中華民國眼科醫學會雜誌
卷期:
45卷4期(2006.12)
頁碼:
448-453
語言:
英語
摘要:
中文摘要PDF
;
英文摘要PDF
目的:報告一個家族滲出性玻璃體視網膜病變的 疾病,探討此疾病的臨床特徵、眼底螢光血管攝影與 治療。 方法:痛例報告 結果:一位9 歲的男性病患主訴雙眼視力模糊6 個月,最佳矯正視力右眼為6/10 左眼為6/20 。眼底 檢查發現雙眼非裂孔性視網膜剝離合併視網膜下織 維化。眼底螢光血管攝影發現周邊血管呈貝扇狀,雙 眼籲側部顯示無血管灌流區域且有新生血管。此病患 無早產見病史且出生體重為正常,出生後並無使用氧 氣治療。經手術治療後,雙眼視網膜均已復位。追蹤 兩年後最佳矯正視力右眼為6/60 左眼為6110 。 結論:視網膜下織維化並非是家族滲出性玻璃體 視網膜病變之常見特徵。早期的手術治療對於此疾病 有較佳之癒後。
Purpose: To repo川a case of familial exudative vitreoretinopathy (FEVR) and discuss the clinical manifestation, angiographic features and treatment of this disease. Method: Interventional case repo吋 Result: A healthy 9-year-old boy complained of progressive blurred vision in both eyes for 6 months. The presenting best-corrected visual acuity (BCVA) was6月o in the right eye and 6/20 in the left eye. Fundoscopy disclosed bilateral non-rhegmatogenous retinal detachment and subretinal fibrosis. Fluorescein angiography revealed avascular area with neovascularization at temporal periphery in both eyes. The temporal retinal vasculature terminated abruptly with scalloped borders adjacent to the avascular zone. He was born in full term without previous exposure to oxygen therapy. After surgical intervention, retina was attached in both eyes. Final BCVA was 6/60 in the right eye and 6/10 in the left eye. Conclusion: Subretinal fibrosis is an unusual feature in FEVR. Early surgical intervention is beneficial to this disease.
本卷期目次
中華民國眼科醫學會雜誌 45卷4期 (2006.12)
OPHTHALMOLOGIC ABNORMALITIES IN TEENAGERS WITH DOWN'S SYNDROME
/
Mei. Ling Liu
;
Yi-Sheng Chang
;
Hon-Chun Cheng
;
Min-Hsiu Shih
;
Sung-Huei Tseng
;
Chia-Lia Teng
CIRCUMSCRIBED CHOROIDAL HEMANGIOMA COMPARISON OF OUTCOMES BY TREATMENT WITH LASER PHOTOCOAGULATION OR TRANSPUPILLARY THERMOTHERAPY
/
Chih-Wei Shih
;
Chang-Hao Yang
;
Chung-May Yang
;
Jen-Shang Huang
;
Chang-Pin Lin
;
Tzyy-Chang Ho
;
Muh-Shy Chen
PARANASAL SINUSITIS FOLLOWING ORBITAL DECOMPRESSION IN PATIENTS WITH GRAVES' OPHTHALMOPATHY
/
Lan Lee
;
Lih Ma
;
Shu-Ya Wu
;
Yueh-Ju Tsai
BREAKDOWN OF THE BLOOD-AQUEOUS BARRIER CAUSED BY ARGON LASER PANRETINAL PHOTOCOAGULATION IN THE RABBIT RETINA
/
Muh-Shy Chen
;
Ching-Chung Chang
;
Szu-Yuan Lin
;
Peng-Chen Wang
;
Ping-Kang Hou
OUTCOMES OF TRABECULECTOMY VERSUS TRABECULECTOMY COMBINED WITH DEEP SCLERECTOMY IN GLAUCOMA PATIENTS──15-MONTH FOLLOW-UP (A PRELIMINARY REPORT)
/
Min-Wen Hsu
;
Shiuh-Liang Hsu
;
Kwou-Yeung Wu
VITRECTOMY WITHOUT INTERNAL LIMITING MEMBRANE PEELING FOR MACULAR RETINOSCHISIS IN HIGHLY MYOPIC EYES
/
Shu-I Yeh
;
Wei-Chun Chan
;
Lee-Jen Chen
配戴各類型隱形眼鏡下人類免疫球蛋白A之比較
/
洪啟庭
;
鍾漢軍
;
陳福安
;
劉峻正
;
陳建同
;
孫昭玲
斜視術後類固醇引起之高眼壓
/
李美侖
;
黃福進
;
史敏秀
JUXTAPAPILLARY CHOROIDAL MELANOMA──A CASE REPORT
/
Feng-Chi Lin
;
Jiann-Torng Chen
;
Chiao-Hong Chen
;
Po-Liang Chen
;
Da-Wen Lu
EOSINOPHILIC LYMPHOGRANULOMA (KIMURA'S DISEASE) OFLACRIMAL GLAND──A CASE REPORT
/
Chia-Ling Lee
;
Pei-Hisn Hu
;
Cheng-Hsien Chang
;
Shiuh-Liang Hsu
;
Ming-Yang Sul
AMNIOTIC MEMBRANE TRANSPLANTATION FOR PERSISTENT CORNEAL EPITHELIAL DEFECT AND ULCERATION
/
Chia-Hung Li
;
Ming-Cheng Tai
;
Jiann-Tomg Chen
;
I Jy-Been Liang
;
Da-Wen Lu
RETINALASTROCYTIC HAMARTOMA COMPLICATED WITH VITREOUS HEMORRHAGE IN TUBEROUS SCLEROSIS
/
Chao-Kung Lu
;
Shih-Jen Chen
;
Fenq-Lih Lee
;
Wen-Ming Hsu
ANTERIOR CAPSULAR PHIMOSIS AFTER SUCCESSFUL SURGERY FOR A PATIENT WITH TRAUMATIC ATARACT: CASE REPORT
/
Chih-Hsien Hsiao
;
Cheng-Jong Chang
;
Po-Liang Chen
CONJUNCTIVAL SEBACEOUS CARCINOMA WITH AN UNUSUAL CLINICAL COURSE──A CASE REPORT
/
Hsiao-Yen Chen
;
Hon-Chun Cheng
;
Sung-Huei Tseng
;
Yi- Chang Tsai
FAMILIAL EXUDATIVE VITREORETINOPATHYA──CASE REPORT
/
Chun-Pin Tsai
;
Der-Chong Tsai
;
Ling-Ing Lau
;
Fenq-Lih Lee
;
Wen-Ming Hsu
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